Congenital Word Deafness and other Defects

Adams Oliver Syndrome and Congenital Deafness

Admas-Oliver syndrome is a rare autosomal dominant disease of congenital development defects association with aplasia cutis. All of 81 reported cases were of 32 group families. These two cases had congenital scalp cutis aplasia with developmental defect and hypoplasia of left foot digits in case 1.Congenital deaf-mute in both can added to the past known findings in this syndrome. Thoracic defor...

Word deafness in Wernicke's aphasia.

Three patients with otherwise typical Wernicke's aphasia showed consistent superiority of visual over auditory comprehension. The precedents for and anatomical basis of a selective auditory deficit in Wernicke's aphasia are discussed, including the relationship to pure word deafness. One implication of spared visual language function may be the use of gesture in language therapy for such patients.

Late congenital syphilitic nerve deafness.

Ritchie Rodger (1945) speaking to this Society classified congenital syphilitic nerve deafness into early and late. He gave two varieties of the early type; a neuritis associated with basal meningitis, and an oto-labyrinthitis. These two early varieties were found to occur in infancy. There is only one late type, a labyrinthitis, which is by far the commonest of all varieties; this usually occu...

Word Deafness and Auditory Cortical Function

A patient who already had Wernicke's aphasia due to a left temporal lobe lesion suffered a severe deterioration specifically of auditory language comprehension, subsequent to right temporal lobe infarction. A detailed comparison of his new condition with his language status before the second stroke revealed that the newly acquired deficit was limited to tasks related to auditory input. Further ...

Word Deafness and Auditory Cortical Function